韦格纳肉芽肿病中的双侧穿孔性巩膜软化症和周边角膜变薄

Bilateral scleromalacia perforans and peripheral corneal thinning in Wegener's granulomatosis.

作者信息

Reddy S C, Tajunisah I, Rohana T

机构信息

Department of Ophthalmology, Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia.

出版信息

Int J Ophthalmol. 2011;4(4):439-42. doi: 10.3980/j.issn.2222-3959.2011.04.22. Epub 2011 Aug 18.

DOI:10.3980/j.issn.2222-3959.2011.04.22

PMID:22553696

原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3340864/

Abstract

A rare case of bilateral scleromalacia perforans, bilateral peripheral corneal thinning (contact lens cornea) and unilateral orbital inflammatory disease in a 50 year old female patient with an indolent form Wegener's granulomatosis(WG) involving lungs and sinuses is reported. The patient survived for 12 years after the initial diagnosis of systemic disease. There was perforation of left globe following trauma and no perforation of the right globe till the last follow up of the patient.

摘要

报告了一例罕见病例，一名50岁女性患者患有惰性型韦格纳肉芽肿（WG）累及肺部和鼻窦，出现双侧穿孔性巩膜软化症、双侧周边角膜变薄（接触镜性角膜）和单侧眼眶炎性疾病。该患者在系统性疾病初步诊断后存活了12年。患者左眼外伤后发生眼球穿孔，直至最后一次随访时右眼未发生穿孔。