Martinez Jaime D, Zendejas Benjamin, Luna Juan Pablo Sánchez, Lopez Joseph, Luna Sergio Sánchez, Mendoza-Sánchez Federico, Farley David R
Universidad Autonoma de Guadalajara, Mexico.
Int J Surg Case Rep. 2012;3(7):333-7. doi: 10.1016/j.ijscr.2012.03.028. Epub 2012 Apr 5.
Paragangliomas are neuroendocrine tumors of the autonomic nervous system that arise from neural crest cells. Paragangliomas are typically extra-adrenal, non-functional and can be discovered incidentally, posing diagnostic and therapeutic challenges.
We present the unusual case of a young man who presented with an acute abdomen secondary to small bowel obstruction, and was found to have an incidental left-sided subdiaphragmatic paraganglioma supplied by a branch of the contralateral right renal artery.
Emergent laparotomy revealed an internal hernia as the source of the small bowel obstruction. Initial attempts to remove an incidental left subdiaphragmatic mass were aborted because of bleeding. Subsequently, after preoperative superselective embolization of the feeding vessel arising from the right renal artery, the mass was successfully resected. Pathology was consistent with a paraganglioma.
This report highlights the rarity of the location and blood supply of an incidental left subdiaphragmatic paraganglioma found in the setting of a small bowel obstruction.
副神经节瘤是起源于神经嵴细胞的自主神经系统神经内分泌肿瘤。副神经节瘤通常位于肾上腺外,无功能,可偶然发现,这给诊断和治疗带来挑战。
我们报告一例罕见病例,一名年轻男性因小肠梗阻导致急腹症就诊,偶然发现左侧膈下副神经节瘤,由对侧右肾动脉分支供血。
急诊剖腹探查显示内疝是小肠梗阻的原因。最初因出血中止了切除偶然发现的左侧膈下肿块的尝试。随后,在对源自右肾动脉的供血血管进行术前超选择性栓塞后,成功切除了肿块。病理结果与副神经节瘤一致。
本报告强调了在小肠梗阻背景下偶然发现的左侧膈下副神经节瘤在位置和血供方面的罕见性。