Chevalier J M, Jimenez M, Sorain F, Choussat A, Baudet E
Service de Cardiologie Pédiatrique, Hôpital Cardiologique du Haut-Levêque, Pessac.
Arch Fr Pediatr. 1990 Aug-Sep;47(7):515-8.
A case of total anomalous pulmonary venous connection is described in a newborn. The pulmonary veins join a common trunk entering portal vein below the diaphragm. The pattern of pulmonary venous connections was identified by two-dimensional Doppler color flow-mapping echocardiography. The common pulmonary venous trunk was anastomosed to the left atrium at the age of 3 weeks but the infant died because of pulmonary hypertension and acute renal insufficiency. The Doppler color echocardiography allows a good preoperative evaluation. The spontaneous prognosis being poor, surgical correction is indicated and should be performed early, even for critically ill neonates. Patients who survive to childhood lead active and full lives.
本文描述了一例新生儿完全性肺静脉异位连接病例。肺静脉汇入一条共同的主干，该主干在膈肌下方进入门静脉。通过二维多普勒彩色血流图超声心动图确定了肺静脉连接的模式。在患儿3周龄时将共同肺静脉主干与左心房进行了吻合，但婴儿因肺动脉高压和急性肾功能不全死亡。多普勒彩色超声心动图可进行良好的术前评估。由于自然预后较差，即使是危重新生儿也应尽早进行手术矫正。存活至儿童期的患者可过上积极充实的生活。
