Fiorino Kristin N, Lestini Brian, Nichols Kim E, Anupindi Sudha A, Maqbool Asim
Division of Gastroenterology, Hepatology and Nutrition, The Children's Hospital of Philadelphia, Perelman, School of Medicine, University of Pennsylvania, Philadelphia, PA 19104, USA.
Case Rep Pediatr. 2011;2011:748543. doi: 10.1155/2011/748543. Epub 2012 Jan 22.
A 10-year-old boy presented with a 3-day history of worsening abdominal pain, fever, emesis and melena. Abdominal ultrasound revealed a right upper quadrant mass that was confirmed by computed tomography angiogram (CTA), which showed an 8 cm well-defined retroperitoneal vascular mass. (123)Iodine metaiodobenzylguanidine ((123)MIBG) scan indicated uptake only in the abdominal mass. Subsequent biopsy revealed a paraganglioma that was treated with chemotherapy. This case represents an unusual presentation of a paraganglioma associated with gastrointestinal (GI) bleeding and highlights the utility of CTA and (123)MIBG in evaluation and treatment.
一名10岁男孩出现腹痛加剧、发热、呕吐和黑便3天的症状。腹部超声显示右上腹有一肿块，计算机断层血管造影（CTA）证实了这一情况，CTA显示一个8厘米边界清晰的腹膜后血管性肿块。碘-间位碘代苄胍（¹²³I-MIBG）扫描显示仅腹部肿块有摄取。随后的活检显示为副神经节瘤，采用化疗进行治疗。该病例代表了副神经节瘤伴有胃肠道出血的一种不寻常表现，并突出了CTA和¹²³I-MIBG在评估和治疗中的作用。
