Department of Pathology, Beijing Friendship Hospital, Capital Medical University, Beijing, China.
Ann Thorac Surg. 2012 Jun;93(6):e145-7. doi: 10.1016/j.athoracsur.2011.12.041.
Mesenchymal cystic hamartoma (MHC) of the lung is a very rare disease with an indolent clinical course and might be easily misdiagnosed as pleuropulmonary blastoma and other uncommon cystic lung lesions. We present a case of a 43-year-old woman who had sudden dyspnea resulting from a spontaneous right-sided pneumothorax. Computed tomography revealed multiple bilateral nodules and cysts of the right lung. Pathologically, the cysts and nodules were composed of primitive mesenchymal cells. The walls of the cysts were lined with normal respiratory epithelium and the nodules were permeated by scattered airways that were also lined with normal respiratory epithelium. Based on the combination of pathologic and clinical features, we made the diagnosis of MHC. One and one-half years after thoracotomy the patient is well without evidence of recurrence.
肺间充质囊性错构瘤(MHC)是一种非常罕见的疾病,具有惰性的临床病程,可能容易误诊为胸膜肺母细胞瘤和其他罕见的囊性肺病变。我们报告一例 43 岁女性患者,因自发性右侧气胸突然出现呼吸困难。计算机断层扫描显示右肺多个双侧结节和囊肿。病理上,囊肿和结节由原始间充质细胞组成。囊肿的壁衬有正常的呼吸上皮,结节内散布着也衬有正常呼吸上皮的气道。基于病理和临床特征的结合,我们做出了 MHC 的诊断。在接受胸腔手术后 1 年半,患者情况良好,无复发迹象。