Department of Medico-Surgical Sciences and Biotechnologies, Polo Pontino-Sapienza University, 04100, Latina, Italy.
Department of Radiological, Oncological and Pathological Sciences, Sapienza, University of Rome, 00161, Rome, Italy.
Gen Thorac Cardiovasc Surg. 2020 Dec;68(12):1573-1578. doi: 10.1007/s11748-020-01370-x. Epub 2020 May 2.
Mesenchymal cystic hamartoma (MCH) of the lung is a rare disease, with an indolent course in the majority of cases. It can be single or multifocal and it is composed of primitive mesenchymal cells admixed with cystic spaces. Only few cases have been reported in the literature, with variable clinical presentation. We describe the case of a huge MCH, presenting with spontaneous pneumothorax in a 65-year-old man. Further, we provide a brief overview of the literature and discuss the differential diagnosis with other entities, and the possible diagnostic pitfalls.
肺间充质囊性错构瘤（MCH）是一种罕见疾病，大多数情况下病程呈惰性。它可以是单发或多发的，由原始间充质细胞与囊性腔隙混合而成。仅有少数病例在文献中报道，临床表现多样。我们描述了一例巨大的 MCH 病例，表现为 65 岁男性自发性气胸。此外，我们还简要概述了文献，并讨论了与其他实体的鉴别诊断，以及可能的诊断陷阱。
