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原发性支气管内浆细胞瘤累及局部淋巴结,并伴有罕见的免疫球蛋白 G 入型单克隆丙种球蛋白血症。

Primary endobronchial plasmacytoma involving local lymph nodes and presenting with rare immunoglobulin G lambda monoclonal gammopathy.

机构信息

Department of Lung Cancer Surgery, Tianjin Key Laboratory of Lung Cancer Metastasis and Tumor Management, Tianjin Medical University General Hospital, Tianjin, China.

出版信息

Can Respir J. 2012 May-Jun;19(3):e28-30. doi: 10.1155/2012/968254.

Abstract

Extramedullary plasmacytoma occurring as a primary pulmonary lesion is rare. The present report describes a 42-year-old Chinese man diagnosed with primary pulmonary plasmacytoma following left lower lobectomy. Of note, an extremely rare immunoglobulin G lambda paraprotein was documented in the patient's serum by immunofixation electrophoresis. The patient has been well, showing no local recurrence or multifocal disease during a 15-month follow-up.

摘要

发生于肺部的髓外浆细胞瘤较为罕见。本报告描述了一例左肺下叶切除术后诊断为原发性肺浆细胞瘤的 42 岁中国男性患者。值得注意的是,免疫固定电泳显示患者血清中存在一种极为罕见的免疫球蛋白 G 入型副蛋白。该患者在 15 个月的随访中情况良好,无局部复发或多灶性疾病。

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