Lightfoot Nicole, Nikfarjam Mehrdad
Department of Pathology, The University of Melbourne, Austin Health, Heidelberg, Melbourne, VIC 3084, Australia.
Case Rep Surg. 2012;2012:382723. doi: 10.1155/2012/382723. Epub 2012 May 29.
Undifferentiated embryonal sarcomas (UESs) are uncommon tumours that are seen predominantly in late childhood. Cases in adults are rare and generally present once a large mass develops and may be mistaken for other tumours. A case of an UES of the liver with an isolated peritoneal metastasis is described. The patient presented with a palpable mass with imaging findings suggestive of a cystic tumour. She had complete surgical resection of the liver mass and isolated peritoneal metastasis. She was tumour-free on imaging at 6 months without adjuvant chemotherapy. An UES should be considered in the differential of large cystic hepatic lesions, with aggressive surgical resection considered when possible.
未分化胚胎性肉瘤(UESs)是一种罕见肿瘤,主要见于儿童晚期。成人病例罕见,通常在形成大肿块后才出现,可能被误诊为其他肿瘤。本文描述了一例肝脏未分化胚胎性肉瘤伴孤立性腹膜转移的病例。患者因可触及肿块就诊,影像学检查结果提示为囊性肿瘤。她接受了肝脏肿块及孤立性腹膜转移灶的完整手术切除。在未接受辅助化疗的情况下,6个月时影像学检查显示她无肿瘤。在鉴别诊断大的肝脏囊性病变时应考虑未分化胚胎性肉瘤,如有可能应考虑积极的手术切除。