Department of Pediatric Surgery, Nemazee Hospital, Shiraz University of Medical Sciences, Shiraz, Iran.
Student Research Committee, Shiraz University of Medical Sciences, Shiraz, Iran.
BMC Gastroenterol. 2022 Jan 3;22(1):2. doi: 10.1186/s12876-021-02076-x.
Undifferentiated embryonal sarcoma of the liver (UESL) is a rare liver tumor accounting for 6-13% of primary liver tumors. Accurate preoperative diagnosis is difficult, with a rather high misdiagnosis rate. Herein, we reported a very large UESL treated with anatomical resection. Our case is amongst the largest pediatric UESLs in the literature.
Herein, we report a 13-year-old girl presenting with right upper quadrant abdominal pain, postprandial vomiting, and abdominal distention, in which radiographic imaging demonstrated a huge UESL (28 × 20 × 12 cm). The patient was treated with partial hepatectomy and the 5 kg tumor was removed. The patient was discharged in good condition, with no significant complaints in her follow-up.
Although different treatment strategies have been reported for UESL cases, anatomical resection is still the main treatment approach, especially for large tumors.
肝未分化胚胎肉瘤（UESL）是一种罕见的肝脏肿瘤，占原发性肝脏肿瘤的 6-13%。准确的术前诊断较为困难，误诊率较高。在此，我们报告了一例经解剖性切除术治疗的非常大的 UESL。我们的病例是文献中最大的儿科 UESL 之一。
本病例报告了一名 13 岁女孩，因右上腹疼痛、餐后呕吐和腹胀就诊，影像学检查显示巨大的 UESL（28×20×12cm）。患者接受了部分肝切除术，切除了 5kg 的肿瘤。患者恢复良好出院，随访时无明显不适。
尽管已有报道提出了不同的 UESL 治疗策略，但解剖性切除术仍是主要的治疗方法，尤其是对于大肿瘤。
