Sung Won-kyung, Au Virginia, Rose Anand
Department of Medical Imaging, Flinders Medical Centre, Adelaide, South Australia, Australia.
J Med Imaging Radiat Oncol. 2012 Jun;56(3):324-7. doi: 10.1111/j.1754-9485.2012.02364.x.
Anomalous pulmonary venous return is an uncommon congenital malformation, and may be partial or total. Partial anomalous pulmonary venous return (PAPVR) is more common than total anomalous pulmonary venous return, and is often associated with other congenital cardiac anomalies. Whilst many patients with PAPVR remain asymptomatic, some may present in later age with symptoms related to left-to-right shunt, right heart failure and pulmonary hypertension. We report two cases of PAPVR detected on Computed Tomography Pulmonary Angiogram (CTPA) for the work up of pulmonary hypertension. The cases demonstrate that, although uncommon, partial anomalous pulmonary venous return can be a contributing factor to pulmonary hypertension and pulmonary veins should be carefully examined when reading a CTPA study.
肺静脉异位引流是一种少见的先天性畸形,可分为部分性或完全性。部分性肺静脉异位引流(PAPVR)比完全性肺静脉异位引流更常见,且常与其他先天性心脏畸形相关。虽然许多PAPVR患者无症状,但有些患者可能在较晚年龄出现与左向右分流、右心衰竭和肺动脉高压相关的症状。我们报告两例在计算机断层扫描肺动脉造影(CTPA)检查肺动脉高压时发现的PAPVR病例。这些病例表明,尽管少见,但部分性肺静脉异位引流可能是肺动脉高压的一个促成因素,在解读CTPA检查结果时应仔细检查肺静脉。