Kerger Laure, Tomescot Andre, Chafai Najim
General and Visceral Surgery Department, Saint Antoine Hospital, St. Antoine, Paris, France.
Ann Vasc Surg. 2012 Aug;26(6):858.e1-2. doi: 10.1016/j.avsg.2011.11.040. Epub 2012 Jun 13.
We describe the case of a 61-year-old woman having a type 1 neurofibromatosis (von Recklinghausen disease), whose acute abdominal pain revealed a voluminous retroperitoneal hemorrhage caused by a 25-mm ruptured inferior mesenteric artery aneurysm. She underwent emergent aneurysm and left colonic resection. This report of a rare digestive artery aneurysm rupture, which added to increasing reports of vascular abnormalities in type 1 neurofibromatosis patients, underlines the need to maintain a high suspicion index of a vascular etiology in case of any abdominal complaint in these patients.
我们描述了一名患有1型神经纤维瘤病（冯雷克林霍增氏病）的61岁女性病例，其急性腹痛显示为一个25毫米破裂的肠系膜下动脉瘤导致大量腹膜后出血。她接受了紧急动脉瘤切除和左半结肠切除术。这份关于罕见的消化动脉动脉瘤破裂的报告，加之1型神经纤维瘤病患者血管异常报告的增加，强调了对于这些患者出现任何腹部不适时，都需要高度怀疑血管病因。
