Kassim Yusra, Penther Dominique, Schneider Pascale, Callat Marie-Paul, Bastard Christian, Vannier Jean-Pierre
Pediatric Hemato-Oncology Department, CHU Charles Nicolle, Rouen, France.
BMJ Case Rep. 2012 Jun 14;2012:bcr0820114663. doi: 10.1136/bcr.08.2011.4663.
The report describes the case of a young male with a malignant teratoma which was followed by an acute megakaryoblastic leukaemia sharing similar chromosomal abnormalities. In leukemic cells, the authors have obtained cytogenetic evidence by fluorescent in situ hybridisation technique suggesting that this leukaemia arose directly from the germ cell tumour (GCT). The patient received allogenic bone marrow transplantation, which unfortunately, did not prevent the patient to relapse with an undifferentiated sarcoma containing rhabdomyosarcoma components, as well as reappearance of a residual teratoma with metastasis. The treatment strategy for malignant transformation of a GCT seems to be unpredictable and should be dictated by the malignant tissue counterpart. Except for acute leukaemia, unresectable or metastatic settings will generally require multi-modal therapy including chemotherapy, in addition to loco regional approaches. Additionally, long or even a life time follow-up is necessary in patients with poor prognostic characteristics.
该报告描述了一名患有恶性畸胎瘤的年轻男性病例,随后发生了伴有相似染色体异常的急性巨核细胞白血病。在白血病细胞中,作者通过荧光原位杂交技术获得了细胞遗传学证据,表明这种白血病直接起源于生殖细胞肿瘤(GCT)。该患者接受了异基因骨髓移植,但不幸的是,这并未阻止患者复发,复发时出现了含有横纹肌肉瘤成分的未分化肉瘤,以及伴有转移的残留畸胎瘤再次出现。GCT恶性转化的治疗策略似乎难以预测,应由恶性组织对应物决定。除急性白血病外,不可切除或转移性情况通常需要多模式治疗,包括化疗以及局部区域治疗方法。此外,预后特征较差的患者需要进行长期甚至终身随访。