Padilla-Fernandez Barbara, Lorenzo-Gomez M Fernanda, Herrero-Polo Manuel, Silva-Abuin Juan M, Martin-Izquierdo Manuela, Antunez-Plaza Patricia
Department of Urology, University Hospital of Salamanca, Salamanca, Spain.
Ann Vasc Surg. 2012 Aug;26(6):859.e1-5. doi: 10.1016/j.avsg.2011.11.043. Epub 2012 Jun 19.
Leiomyosarcoma of the inferior vena cava (IVC) is a rare tumor arising from its smooth muscle cells.
We report the case of a 38-year-old woman presenting with back pain and weight loss who was diagnosed with a 22-cm leiomyosarcoma of the right IVC and thrombosis of the left IVC. The patient is alive and free of recurrence a year after radical tumor resection with removal of the affected IVC, reconstruction with polytetrafluoroethylene prosthetic graft, and anastomosis of both right and left IVC.
Leiomyosarcoma is a rare and aggressive tumor with a deceitful course. Radical surgical en bloc resection is the mainstay of treatment for IVC leiomyosarcomas. For an adequate restoration of venous return, complex vascular repair may be necessary.
下腔静脉平滑肌肉瘤是一种起源于其平滑肌细胞的罕见肿瘤。
我们报告了一例38岁女性病例，该患者因背痛和体重减轻就诊，被诊断为右下腹下腔静脉22厘米平滑肌肉瘤并伴有左下腹下腔静脉血栓形成。患者在接受根治性肿瘤切除（切除受累的下腔静脉）、用聚四氟乙烯人工血管进行重建以及左右下腹下腔静脉吻合术后一年，仍存活且无复发。
平滑肌肉瘤是一种罕见且侵袭性强的肿瘤，病程隐匿。根治性整块手术切除是下腔静脉平滑肌肉瘤的主要治疗方法。为充分恢复静脉回流，可能需要进行复杂的血管修复。
