Koç Zehra Pinar, Akarsu Saadet, Balci Tansel, Unal Kemal
Department of Nuclear Medicine, Fırat University Hospital, Elazig, Turkey.
BMJ Case Rep. 2012 Jun 21;2012:bcr0320126026. doi: 10.1136/bcr-03-2012-6026.
Haemophagocytic lymphohistiocytosis (HLH) is a rare immune disorder that predominantly affects macrophages and T lymphocytes and leads to multiple organ disease and death. The characteristic pathological finding in the bone marrow and the other affected tissues is haemophagocytosis of macrophages (macrophages digesting erythrocyte). Primary (hereditary) and secondary (acquired) forms of the disease are present. A patient with documented HLH disease revealed by positron emission tomography/CT is reported in this paper.
噬血细胞性淋巴组织细胞增生症（HLH）是一种罕见的免疫紊乱疾病，主要影响巨噬细胞和T淋巴细胞，并导致多器官疾病和死亡。骨髓及其他受累组织的特征性病理表现是巨噬细胞的噬血细胞现象（巨噬细胞吞噬红细胞）。该疾病有原发性（遗传性）和继发性（获得性）两种形式。本文报道了一例经正电子发射断层扫描/计算机断层扫描（PET/CT）确诊为HLH疾病的患者。
