Department of Pulmonology, University of Medical Sciences, Poznan, Poland.
Adv Exp Med Biol. 2013;755:149-54. doi: 10.1007/978-94-007-4546-9_20.
Scleroderma typically manifests as fibrosis of the skin, but may also involve other organs, particularly the lungs. Interstitial lung disease and functional abnormalities are observed in the majority of patients. The aim of this study was to evaluate radiological changes in the lungs and their correlation with functional disorders in scleroderma patients. The study was conducted in 37 scleroderma patients (F/M-31/6). High resolution computed tomography (HRCT), Warrick score system and spirometry, body plethysmography, and lung diffusion examinations (DLco) were performed. The HRCT showed septal and subpleural lines in 70%, ground-glass opacities in 51%, and honeycomb lungs in 30% of the cases. The DLco values were decreased in 92% of the patients. Total lung capacity (TLC) showed a restrictive pattern in 24% of the patients, and only in 11% of them obstruction predominated. The Warrick score correlated inversely with both DLco (r=0.36; p>0.05). Interstitial lung disease often coexists with scleroderma and is accompanied by functional lung abnormalities.
硬皮病通常表现为皮肤纤维化,但也可能涉及其他器官,特别是肺部。大多数患者存在间质性肺疾病和功能异常。本研究旨在评估硬皮病患者肺部的影像学变化及其与功能障碍的相关性。该研究纳入了 37 名硬皮病患者(F/M-31/6)。进行了高分辨率计算机断层扫描(HRCT)、Warrick 评分系统以及肺量测定、体积描记法和肺弥散功能检查(DLco)。HRCT 显示 70%存在间隔线和胸膜下线,51%存在磨玻璃影,30%存在蜂窝肺。92%的患者存在 DLco 值降低。24%的患者总肺容量(TLC)呈限制性模式,仅 11%的患者以阻塞为主。Warrick 评分与 DLco 呈负相关(r=0.36;p>0.05)。间质性肺疾病常与硬皮病并存,并伴有肺功能异常。