Loggos Spiros, Kondrafouris Konstandinos, Oikonomopoulos George, Mitropoulos Fotios
Department of Paediatric and Congenital Cardiac Surgery, Onassis Heart Centre, Kallithea, Athens, Greece.
Interact Cardiovasc Thorac Surg. 2012 Nov;15(5):909-11. doi: 10.1093/icvts/ivs324. Epub 2012 Jul 25.
We present the interesting case of a 15-year old boy with a monophasic synovial sarcoma (MSS) of the mediastinum, which was infiltrating the right heart chambers and the inferior vena cava (IVC). A radical excision was performed, with extensive reconstruction of the heart, under deep hypothermic circulatory arrest. Radical surgical excision is considered to be the treatment of choice for these lesions, as chemotherapy and radiotherapy have little effect. Unfortunately, the patient and his parents refused any further consultation with an oncologist and, although there was no recurrence at 12 months following the procedure, at 24 months we were informed of his death due to the tumour appearing on the left cardiac chambers with subsequent multi-organ failure.
我们报告了一例有趣的病例，一名15岁男孩患有纵隔单相滑膜肉瘤（MSS），该肿瘤已侵犯右心腔和下腔静脉（IVC）。在深低温循环停搏下进行了根治性切除，并对心脏进行了广泛重建。根治性手术切除被认为是这些病变的首选治疗方法，因为化疗和放疗效果甚微。不幸的是，患者及其父母拒绝与肿瘤学家进行任何进一步咨询，尽管术后12个月没有复发，但在24个月时，我们得知他因肿瘤出现在左心腔并随后出现多器官衰竭而死亡。
