Department of Plastic Surgery, Loma Linda University Medical Center, 11175 Campus Street, Suite 21126, Loma Linda, CA 92354, USA.
J Plast Reconstr Aesthet Surg. 2013 Feb;66(2):281-6. doi: 10.1016/j.bjps.2012.06.024. Epub 2012 Aug 4.
Massive localised lymphoedema (MLL) is a benign lymphoproliferative soft-tissue overgrowth in the morbidly obese patient. The diagnosis may be challenging, and is a form of secondary lymphoedema, often described as idiopathic scrotal elephantiasis. The lesion presents as a large mass in the morbidly obese, and patients seek treatment late in the disease course due to limitation of daily living or excoriation and wound breakdown. Resection, followed by reconstruction, is indicated in these cases. We present a unique case of a morbidly obese 52-year-old male with massive enlargement of the scrotum present for several years duration, despite massive weight loss (88.85 kg) from gastric bypass surgery and no other identifiable cause of lymphoedema. Scrotal lymphoedematous tissue was resected and scrotal reconstruction with a novel posterior fasciocutaneous flap from the scrotum was performed in addition to penile reconstruction with a skin graft and local fasciocutaneous flaps as well as a panniculectomy. Histologically, the tissue was characterised by marked oedema with dermal fibrosis and patchy mild perivascular chronic inflammation. Postoperative follow-up revealed wound integrity and patient satisfaction with the outcome. MLL is an important disease process with distinct clinical and histopathologic characteristics that often requires complex reconstruction. Although there are several opposing classification schema, we propose the incorporation of idiopathic scrotal elephantiasis into the diagnostic category of MLL.
巨大局部性淋巴水肿(MLL)是病态肥胖患者中良性淋巴增生性软组织过度生长的一种疾病。这种疾病的诊断可能具有挑战性,它是继发性淋巴水肿的一种形式,通常被描述为特发性阴囊象皮病。病变表现为病态肥胖患者的巨大肿块,由于日常生活受限或擦伤和伤口破裂,患者在疾病晚期才寻求治疗。在这些情况下,建议进行切除,然后进行重建。我们报告了一例独特的病例,一名 52 岁的病态肥胖男性,阴囊肿大数年,尽管接受了胃旁路手术后体重减轻了 88.85 公斤,但仍无其他可识别的淋巴水肿原因。我们切除了阴囊的淋巴水肿组织,并进行了阴囊重建,使用了一种新颖的来自阴囊的后侧筋膜皮瓣,同时还进行了阴茎重建,包括皮肤移植和局部筋膜皮瓣以及腹部脂肪切除术。组织学上,该组织的特征是明显的水肿,伴有皮肤纤维化和斑片状轻度血管周围慢性炎症。术后随访显示伤口完整,患者对结果满意。MLL 是一种具有独特临床和组织病理学特征的重要疾病过程,通常需要复杂的重建。尽管有几种相反的分类方案,但我们建议将特发性阴囊象皮病纳入 MLL 的诊断类别。