Soyer P, Dobbelaere P, Reizine D, Ferquel C
Service de Radiologie, Institut Gustave-Roussy, Villejuif.
J Neuroradiol. 1990;17(3):222-6.
Basal encephaloceles are uncommon congenital malformations occurring with an estimated frequency of one case in 35,000 births. They are frequently occult since they protrude into the orbit, nasal cavity, nasopharynx or paranasal sinuses. Basal encephaloceles are divided into five anatomical types. We report a case of transsphenoidal encephalocele which differed from the classical type in that it protruded through a congenital defect in the greater wing of the sphenoid bone. This case had an unusual clinical presentation, being responsible for trigeminal neuralgia and associated with an angioma of the soft palate.
基底脑膨出是一种罕见的先天性畸形，估计发病率为35000例出生中有1例。由于它们突入眼眶、鼻腔、鼻咽或鼻窦，所以常常隐匿。基底脑膨出分为五种解剖类型。我们报告一例经蝶骨脑膨出病例，它与经典类型不同，是通过蝶骨大翼的先天性缺损突出。该病例有不寻常的临床表现，引起三叉神经痛并伴有软腭血管瘤。
