Jabre A, Tabaddor R, Samaraweera R
Department of Neurosurgery, Boston University and Boston Veterans Administration Medical Center, Boston, Massachusetts 02118, USA.
Surg Neurol. 2000 Aug;54(2):183-7; discussion 187-8. doi: 10.1016/s0090-3019(00)00270-6.
Transsphenoidal meningoencephalocele is a rare congenital anomaly, reported only in 14 adult patients. It may be subdivided into intrasphenoidal, extending into the sphenoid sinus, and true transsphenoidal, traversing the floor of the sinus and protruding into the nasal cavity or nasopharynx.
We present the eighth case of true transsphenoidal meningoencephalocele reported in an adult. We review the literature and highlight the differences in clinical presentation and therapeutic management between patients with intrasphenoidal and true transsphenoidal meningoencephalocele.
Adult patients with intrasphenoidal meningoencephalocele often present with rhinorrhea and should be considered for transsphenoidal repair, whereas patients with true transsphenoidal meningoencephalocele should not undergo surgery, in view of the complex anatomy and the slow progression of symptoms.
经蝶窦脑膜脑膨出是一种罕见的先天性异常，仅在14例成年患者中报道过。它可分为蝶窦内型，即延伸至蝶窦内，以及真正的经蝶窦型，即穿过蝶窦底部并突入鼻腔或鼻咽部。
我们报告了第8例成年患者的真正经蝶窦脑膜脑膨出病例。我们回顾了文献，并强调了蝶窦内型和真正经蝶窦型脑膜脑膨出患者在临床表现和治疗管理上的差异。
蝶窦内型脑膜脑膨出的成年患者常出现鼻漏，应考虑经蝶窦修复，而真正经蝶窦型脑膜脑膨出的患者由于解剖结构复杂且症状进展缓慢，不应接受手术治疗。
