Eftekhari F, Erly W K, Jaffe N
Division of Diagnostic Imaging, University of Texas M. D. Anderson Cancer Center, Houston.
Pediatr Radiol. 1990;21(1):39-42. doi: 10.1007/BF02010812.
Two new cases of malignant rhabdoid tumor of the kidney (RTK) in childhood are reported. Both presented with large abdominal masses and developed hypertension and one became hypercalcemic during the course of the disease. In each case disseminated disease and death occurred within three months of diagnosis. The findings on imaging consisted of large renal masses with a central site of origin, distant metastases at the time of presentation, and a subcapsular fluid collection in one of the two patients. The clinical and imaging features of RTK may suggest this diagnosis when faced with a primary renal neoplasm in childhood.
报告了两例儿童期肾恶性横纹肌样瘤（RTK）的新病例。两例均表现为腹部巨大肿块并出现高血压，其中一例在病程中出现高钙血症。每例在诊断后三个月内均发生播散性疾病并死亡。影像学检查结果包括起源于中央部位的巨大肾脏肿块、就诊时的远处转移以及两名患者中的一例出现包膜下液体积聚。当面对儿童期原发性肾肿瘤时，RTK的临床和影像学特征可能提示该诊断。
