Palermo Mariano, Mastronardi Luis M, García Rafael H, Solari Ignacio, Tarsitano Francisco J
Department of Gastrointestinal Surgery, Hospital Nacional Prof A. Posadas.
Acta Gastroenterol Latinoam. 2012 Jun;42(2):131-4.
Rhabdomyosarcomas are rare and malignant tumors. There have been reported two histological types of gastric rhabdomyosarcomas, the pleomorphic and embryonal cell types. We report the case of a 53-year-old male with endoscopic diagnosis of a Bormann type III ulcer which revealed a gastric primary rhabdomyosarcoma. Ultrasound showed two liver lesions, two hepatic pedicle lymph nodes and a huge primary gastric tumor. CT scan revealed a primary gastric tumor. The patient is submitted to a distal gastrectomy with a Billroth II reconstruction and a resection of the distal liver metastases at segment IV The patient was discharged uneventfully on the eighth postoperative day. The gold standard for a final diagnoses is the immuno-histochemical staining of the endoscopic biopsy. There is very little information on the results of chemotherapy and the surgical treatment is the best choice.
横纹肌肉瘤是罕见的恶性肿瘤。已有报道称胃横纹肌肉瘤有两种组织学类型，即多形性和胚胎细胞型。我们报告一例53岁男性患者，内镜诊断为Borrmann III型溃疡，结果显示为原发性胃横纹肌肉瘤。超声检查发现肝脏有两个病灶、两个肝蒂淋巴结以及一个巨大的原发性胃肿瘤。CT扫描显示有原发性胃肿瘤。该患者接受了毕罗II式重建的远端胃切除术以及IV段远端肝转移灶切除术。患者术后第八天顺利出院。最终诊断的金标准是内镜活检的免疫组织化学染色。关于化疗结果的信息非常少，手术治疗是最佳选择。
