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法洛四联症:外科手术视角

Tetralogy of fallot: a surgical perspective.

作者信息

Karl Tom R

机构信息

Cardiac Surgical Unit, Mater Children's Hospital, Queensland Paediatric Cardiac Service, Australia.

出版信息

Korean J Thorac Cardiovasc Surg. 2012 Aug;45(4):213-24. doi: 10.5090/kjtcs.2012.45.4.213. Epub 2012 Aug 3.

DOI:10.5090/kjtcs.2012.45.4.213
PMID:22880165
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC3413825/
Abstract

Tetralogy of Fallot (TOF) is an index lesion for all paediatric and congenital heart surgeons. In designing an appropriate operation for children with TOF, the predicted postoperative physiology must be taken into account, both for the short and long term. A favourable balance between pulmonary stenosis (PS) and pulmonary insufficiency (PI) may be critical for preservation of biventricular function. A unified repair strategy to limit both residual PS and PI is presented, along with supportive experimental evidence. A strategy for dealing with coronary anomalies and some comments regarding best timing of operation are also included.

摘要

法洛四联症(TOF)是所有小儿及先天性心脏病外科医生的标志性病变。在为TOF患儿设计合适的手术时,必须考虑到术后短期和长期的预期生理状况。肺动脉狭窄(PS)和肺动脉瓣关闭不全(PI)之间的良好平衡对于保留双心室功能可能至关重要。本文提出了一种统一的修复策略,以限制残余PS和PI,并提供了支持性实验证据。还包括处理冠状动脉异常的策略以及关于最佳手术时机的一些评论。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/d46654698d96/kjtcs-45-213-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/d3fd2fd5a91f/kjtcs-45-213-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/f7f7b981257c/kjtcs-45-213-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/009f14f816a5/kjtcs-45-213-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/98e3a3866e9b/kjtcs-45-213-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/730473f56041/kjtcs-45-213-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/b457b823f1ed/kjtcs-45-213-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/fded6e3cc302/kjtcs-45-213-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/d46654698d96/kjtcs-45-213-g008.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/d3fd2fd5a91f/kjtcs-45-213-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/f7f7b981257c/kjtcs-45-213-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/009f14f816a5/kjtcs-45-213-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/98e3a3866e9b/kjtcs-45-213-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/730473f56041/kjtcs-45-213-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/b457b823f1ed/kjtcs-45-213-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/fded6e3cc302/kjtcs-45-213-g007.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/9a70/3413825/d46654698d96/kjtcs-45-213-g008.jpg

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本文引用的文献

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Unrepaired tetralogy of fallot in an 85-year-old man.一名85岁男性的未修复法洛四联症。
Congenit Heart Dis. 2012 Sep-Oct;7(5):E78-81. doi: 10.1111/j.1747-0803.2012.00642.x. Epub 2012 Apr 3.
2
Timing and technique of pulmonary valve replacement in the patient with tetralogy of Fallot.法洛四联症患者肺动脉瓣置换的时机与技术
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2012;15(1):27-33. doi: 10.1053/j.pcsu.2012.01.007.
3
Valve-sparing options in tetralogy of Fallot surgery.法洛四联症手术中的保留瓣膜术式
Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2012;15(1):24-6. doi: 10.1053/j.pcsu.2012.01.006.
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Tetralogy of Fallot repair: ready for a new paradigm.法洛四联症修复术:迎接新范式
J Thorac Cardiovasc Surg. 2012 Jun;143(6):1305-6. doi: 10.1016/j.jtcvs.2012.01.076. Epub 2012 Feb 18.
5
Impact of pressure load caused by right ventricular outflow tract obstruction on right ventricular volume overload in patients with repaired tetralogy of Fallot.右心室流出道梗阻引起的压力负荷对法洛四联症根治术后右心室容量超负荷的影响。
J Thorac Cardiovasc Surg. 2012 Jun;143(6):1299-304. doi: 10.1016/j.jtcvs.2011.12.033. Epub 2012 Jan 12.
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Functional health status in adult survivors of operative repair of tetralogy of fallot.成人法洛四联症根治术后患者的功能性健康状况。
Am J Cardiol. 2012 Mar 15;109(6):873-80. doi: 10.1016/j.amjcard.2011.10.051. Epub 2012 Jan 13.
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Variation in outcomes for benchmark operations: an analysis of the Society of Thoracic Surgeons Congenital Heart Surgery Database.基准手术结果的变化:胸外科医师学会先天性心脏病外科学数据库分析。
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Relation of left ventricular end diastolic pressure to right ventricular end diastolic volume after operative treatment of tetralogy of fallot.法洛四联症术后左心室舒张末期压力与右心室舒张末期容积的关系。
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