Yilmaz Sedat, Tezel Kutay, Ocal Ramazan, Ilıca Turan, Cinar Muhammet, Erdem Hakan, Pay Salih, Dinc Ayhan, Simsek Ismail
Division of Rheumatology, Gulhane School of Medicine, Ankara, Turkey.
Bull NYU Hosp Jt Dis. 2012;70(2):120-3.
Although neurological involvement in Behçet's disease is not so uncommon, isolated spinal cord disease is quite rare and reported to be observed in about 2% of all cases with neurological involvement. Here we report a Behçet's patient with spinal cord disease presented with anterior spinal cord syndrome. This rare syndrome is caused by hypoperfusion of the anterior spinal artery and to our knowledge has not been previously reported in patients with Behçet's disease. This report defines the characteristic clinical features of this entity and emphasizes the importance of early immunosuppressive treatment and initiation of rehabilitation.
尽管贝赫切特病的神经系统受累并不少见,但孤立性脊髓疾病相当罕见,据报道在所有神经系统受累病例中约占2%。在此,我们报告一例患有脊髓疾病并表现为脊髓前动脉综合征的贝赫切特病患者。这种罕见的综合征是由脊髓前动脉灌注不足引起的,据我们所知,此前尚未在贝赫切特病患者中报道过。本报告明确了该病症的特征性临床特点,并强调了早期免疫抑制治疗和启动康复治疗的重要性。