脾梗死伴多脾综合征及内脏反位。
Splenic infarct with polysplenia syndrome and situs inversus.
作者信息
Suthar Tejas, Banker Hiral, Shah Mukesh, Thakkar Gurudatt
机构信息
Radiology Department, VSGH, Ahmedabad, Gujarat, India.
出版信息
BMJ Case Rep. 2012 Aug 14;2012:bcr0220125831. doi: 10.1136/bcr.02.2012.5831.
Abstract
A rare case of spontaneous splenic infarction with polysplenia and situs inversus is presented. The diagnosis was made by ultrasound and confirmed by CT which showed multiple aberrant right-sided spleens with situs inversus and one of the spleen showing low attenuation areas representing infarct. Polysplenia syndrome is a rare entity associated with heterotaxy syndromes, congenital cyanotic heart diseases, billiary atresia, intestinal malrotation, immotile cilia syndrome, annular or short pancreas, preduodenal portal vein and vena caval anomalies.
摘要
本文报告一例罕见的自发性脾梗死合并多脾畸形及内脏反位病例。通过超声做出诊断，并经CT证实，CT显示多个位于右侧的异常脾脏伴内脏反位，其中一个脾脏有代表梗死的低密度区。多脾综合征是一种罕见的疾病，与内脏异位综合征、先天性青紫型心脏病、胆道闭锁、肠旋转不良、纤毛不动综合征、环状或短胰腺、十二指肠前门静脉和腔静脉异常有关。
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