Graça Susana Alexandra Rodrigues, Sequeira Hugo, Coelho Gustavo, Costa Horácio
Department of General Surgery, Centro Hospitalar Gaia/Espinho, EPE, Gaia, Portugal.
BMJ Case Rep. 2012 Aug 21;2012:bcr0220125914. doi: 10.1136/bcr-02-2012-5914.
Adenoid cystic carcinoma (ACC) is a rare malignant neoplasm, arising from glandular tissues, found mainly in the head and neck. Generally, it presents insidiously but can behave aggressively making its course unpredictable. Surgery and adjuvant radiotherapy continue to be the cornerstone for its treatment. ACC remains extremely difficult to treat. The authors report a case of a 37-year-old woman with bloody rhinorrhea for 6 months. She was diagnosed with a left nasal cavity lesion that was biopsied, and the anatomopathological result showed ACC. The patient was submitted to a left extended maxillectomy, microsurgical reconstruction and radiotherapy.
腺样囊性癌（ACC）是一种罕见的恶性肿瘤，起源于腺组织，主要发生在头颈部。一般来说，它起病隐匿，但可能侵袭性生长，其病程难以预测。手术和辅助放疗仍然是其治疗的基石。ACC仍然极难治疗。作者报告了一例37岁女性，有6个月的血性鼻漏症状。她被诊断为左侧鼻腔病变并进行了活检，解剖病理学结果显示为腺样囊性癌。该患者接受了左侧扩大上颌骨切除术、显微外科重建和放疗。
