Belaj Klara, Gary Thomas, Eller Philipp, Deutschmann Hannes, Beham-Schmid Christine, Gorkiewicz Gregor, Brodmann Marianne
Division of Angiology, Department of Internal Medicine, Medical University of Graz, Austria.
Vasa. 2012 Sep;41(5):371-4. doi: 10.1024/0301-1526/a000224.
Kikuchi Fujimoto disease (KFD) is a rare form of lymphadeopathy with systemic symptoms. We present a case of a 31-year-old female farmer who was admitted to the emergency ward because of swelling of the left arm. Upper extremity venous thrombosis due to local compression of lymph nodes was diagnosed. The histological workup of lymph node biopsy showed histiocytic necrotizing lymphadenitis which is a typical sign of KFD. Anticoagulant treatment for the venous thrombosis was initiated. As KFD is often associated with a transition to systemic lupus erythematosus follow up visits are scheduled in our outpatient clinic.
菊池富士本病(KFD)是一种伴有全身症状的罕见淋巴结病。我们报告一例31岁女性农民,因左臂肿胀入住急诊病房。诊断为淋巴结局部压迫导致的上肢静脉血栓形成。淋巴结活检的组织学检查显示组织细胞坏死性淋巴结炎,这是KFD的典型表现。开始对静脉血栓形成进行抗凝治疗。由于KFD常与系统性红斑狼疮的转变相关,我们的门诊安排了随访。