Departement of Neurosurgery, Faculty of Medicine, Geneva University Hospitals, Geneva, Switzerland.
Acta Neurochir (Wien). 2012 Nov;154(11):2109-13; discussion 2113. doi: 10.1007/s00701-012-1438-6. Epub 2012 Sep 7.
A 39-year old man came to our outpatient clinic with long history of unspecific symptoms and signs. Cerebral MRI showed herniation of the cerebellar tonsils of more than 1 cm below the foramen magnum and a triventricular hydrocephalus. A diagnosis of Chiari I malformation was retained. After an osteo-dural decompression of the posterior fossa, post-operative MRI revealed an aqueductal stenosis with triventricular hydrocephalus. An endoscopic-third- ventriculostomy showed an idiopathic stenosis of the right foramen of Monro. Residual symptoms and persistence of biventricular hydrocephalus justified a ventriculo-peritoneal shunt. Aqueductal and foramina of Monro stenosis can mimick a Chiari I malformation.
一位 39 岁男性因长期存在不典型症状和体征来我院门诊就诊。头颅 MRI 显示小脑扁桃体下疝超过 1cm,三脑室脑积水。诊断为 Chiari I 畸形。行颅后窝骨-硬脑膜减压术后,术后 MRI 显示导水管狭窄伴三脑室脑积水。内镜第三脑室造瘘术显示右侧 Monro 孔狭窄。残留症状和双侧脑室脑积水持续存在,需要行脑室-腹腔分流术。导水管和 Monro 孔狭窄可以模拟 Chiari I 畸形。