在COS7细胞中表达所证实的人艾杜糖醛酸-2-硫酸酯酶突变导致的活性降低和蛋白质加工改变 - Suppr

Decreasing activity and altered protein processing of human iduronate-2-sulfatase mutations demonstrated by expression in COS7 cells.

作者信息

Charoenwattanasatien Ratana, Cairns James R Ketudat, Keeratichamroen Siriporn, Sawangareetrakul Phannee, Tanpaiboon Pranoot, Wattanasirichaigoon Duangrurdee, Pangkanon Suthipong, Svasti Jisnuson, Champattanachai Voraratt

机构信息

Laboratory of Biochemistry, Chulabhorn Research Institute, Bangkok, 10210, Thailand.

出版信息

Biochem Genet. 2012 Dec;50(11-12):990-7. doi: 10.1007/s10528-012-9538-9. Epub 2012 Sep 19.

DOI:10.1007/s10528-012-9538-9

PMID:22990955

Abstract

摘要

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Decreasing activity and altered protein processing of human iduronate-2-sulfatase mutations demonstrated by expression in COS7 cells.在COS7细胞中表达所证实的人艾杜糖醛酸-2-硫酸酯酶突变导致的活性降低和蛋白质加工改变

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Decreasing activity and altered protein processing of human iduronate-2-sulfatase mutations demonstrated by expression in COS7 cells.

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