Department of Obstetrics and Gynecology, University of Virginia, Charlottesville, VA 22903, USA.
Obstet Gynecol. 2012 Oct;120(4):948-51. doi: 10.1097/AOG.0b013e318265e35a.
Herlyn-Werner-Wunderlich syndrome is defined by uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. We report the presentation, radiographic findings, and outcomes of three patients with Herlyn-Werner-Wunderlich syndrome who underwent surgical management at a tertiary care academic medical center.
Two patients were diagnosed by magnetic resonance imaging and one by ultrasonography. All three underwent successful transvaginal septoplasty and drainage of the hematocolpos and hematometra. One required septoplasty revision with temporary vaginal stent placement.
Herlyn-Werner-Wunderlich syndrome is a rare condition. The most urgent concern is the obstruction of menstrual effluent. Unlike an isolated transverse vaginal septum, the vaginal septum with Herlyn-Werner-Wunderlich syndrome is parallel to the patent vaginal canal, less pliable, and closer to the cervix. These anatomical differences result in pronounced distortion with significant diagnostic and surgical challenges.
Herlyn-Werner-Wunderlich 综合征的定义为子宫双角、阴道横隔伴同侧肾发育不全。我们报告了在一家三级学术医疗中心接受手术治疗的三例 Herlyn-Werner-Wunderlich 综合征患者的临床表现、影像学发现和结果。
两名患者通过磁共振成像诊断，一名患者通过超声检查诊断。所有三例患者均成功地进行了经阴道隔切开术和阴道积血、积脓的引流。其中一例需要进行阴道隔切开术修正，并暂时放置阴道支架。
Herlyn-Werner-Wunderlich 综合征是一种罕见的疾病。最紧急的问题是月经血流出受阻。与孤立的横向阴道隔不同，Herlyn-Werner-Wunderlich 综合征的阴道隔与通畅的阴道通道平行，缺乏柔韧性，且更接近宫颈。这些解剖学差异导致明显的扭曲，存在显著的诊断和手术挑战。
