Karaca Leyla, Pirimoglu Berhan, Bayraktutan Ummugulsum, Ogul Hayri, Oral Akgun, Kantarci Mecit
Department of Radiology, Ataturk University, School of Medicine, Erzurum, Turkey.
Department of Pediatric Surgery, Ataturk University, School of Medicine, Erzurum, Turkey.
J Emerg Med. 2015 Mar;48(3):e73-5. doi: 10.1016/j.jemermed.2014.09.064. Epub 2014 Dec 8.
Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon variant of Müllerian duct anomalies, consisting of uterine didelphys, obstructed hemivagina, and ipsilateral renal agenesis. It usually presents in a post-pubertal adolescent or adult woman in whom hematometrocolpos produces a pronounced mass effect and pain on the side of the obstructed hemivagina.
We report the case of a 13-year-old girl who presented to the emergency radiology department with sudden onset of severe pain at the right lower quadrant of the abdomen; imaging confirmed the diagnosis of HWW syndrome. WHY SHOULD AN EMERGENCY PHYSICIAN BE AWARE OF THIS?: When unilateral renal agenesis and uterus didelphys coexist, the first thing that the physician should remember is to confirm or refute the presence of a blind vagina for diagnosis of HWW syndrome.
赫林-韦纳-温德利希（HWW）综合征是苗勒管异常的一种罕见变异型，由双子宫、梗阻性半阴道和同侧肾缺如组成。它通常出现在青春期后或成年女性中，积血积脓的子宫阴道造成明显的占位效应，并引起梗阻性半阴道一侧疼痛。
我们报告了一名13岁女孩的病例，她因突发严重右下腹痛就诊于急诊放射科；影像学检查确诊为HWW综合征。为什么急诊医生应该了解这个病？：当单侧肾缺如和双子宫并存时，医生首先应记住要确认或排除盲端阴道的存在，以诊断HWW综合征。
