Arikawa K, Morishita Y, Watanabe K, Taira A
Second Department of Surgery, Kagoshima University School of Medicine.
Kyobu Geka. 1990 Jan;43(1):80-2.
A rare case of pure severe aortic regurgitation (AR) accompanied with congenital bicuspid aortic valve is presented. A 36-year-old female was admitted with rapid development of congestive heart failure. Examinations clarified severe AR with congenital bicuspid valve. Either calcification or vegetation on the valve was completely denied. At operation, both leaflets were apart from each other with a distance of 7 mm at the anterior commissura. A mechanical valve (Björk-Shiley 23A) was sutured and she has been well. Pathological study of the resected leaflets revealed neither calcium deposit nor finding of infection but collagenous fibrous tissue with focal mucinous degeneration. A few cases of AR with bicuspid aortic valve have been reported in patients of annuloaortic ectasia. The partial annular ectasia was suspected as the cause of solitary aortic regurgitation with bicuspid aortic valve in our case.
本文报告一例罕见的单纯严重主动脉瓣反流（AR）合并先天性二叶式主动脉瓣病例。一名36岁女性因充血性心力衰竭快速进展入院。检查明确为先天性二叶式瓣膜导致的严重AR。瓣膜上未发现钙化或赘生物。手术时，两个瓣叶在前联合处相互分离，距离为7毫米。植入了一枚机械瓣膜（Björk-Shiley 23A），患者术后情况良好。切除瓣叶的病理研究显示既无钙沉积也无感染迹象，仅有伴有局灶性黏液样变性的胶原纤维组织。已有一些关于二叶式主动脉瓣合并主动脉瓣反流的病例报道，这些病例患者存在主动脉根部扩张。在我们的病例中，部分主动脉根部扩张被怀疑是导致单纯二叶式主动脉瓣主动脉瓣反流的原因。
