Sahin Tayfun, Bozyel Serdar, Acar Eser, Bildirici Ulas, Yavuz Sadan, Baris Ozgur, Ural Ertan, Ural Dilek
Department of Cardiology, Medical Faculty of Kocaeli University, Kocaeli, Turkey.
Cardiovasc J Afr. 2012 Sep 12;23(8):e15-8. doi: 10.5830/CVJA-2012-037.
A rare congenital anomaly of the coronary arteries, in which the left coronary arterial system starts from the arteria pulmonalis, is known as Bland-White-Garland (BWG) syndrome. Isolated left anterior descending (LAD) or circumflex (Cx) arteries originating from the pulmonary artery are even more rare. These anomalies may cause myocardial ischaemia, myocardial infarction, arrhythmia and sudden death. Even if the patient is asymptomatic, he/she should undergo corrective surgery. Here we present the case of an 18-year-old male who survived sudden cardiac arrest during exercise. We identified intra-myocardial blood flow from transthoracic echocardiography, and performed coronary and computed tomographic (CT) angiography, which showed that all the coronary arteries were ectatic and curly and there were disseminated collaterals among the coronary arteries. We diagnosed 'anomalous left coronary artery from the pulmonary artery' (ALCAPA) syndrome, as additionally, the LAD originated from the pulmonary artery. We treated the patient with a left internal mammarian artery - left anterior descending artery (LIMA-LAD) graft.
一种罕见的冠状动脉先天性异常,即左冠状动脉系统起源于肺动脉,被称为布兰德 - 怀特 - 加兰(BWG)综合征。孤立的起源于肺动脉的左前降支(LAD)或回旋支(Cx)动脉更为罕见。这些异常可能导致心肌缺血、心肌梗死、心律失常和猝死。即使患者无症状,也应接受矫正手术。在此,我们报告一例18岁男性患者,他在运动期间心脏骤停后幸存。我们通过经胸超声心动图识别出心肌内血流,并进行了冠状动脉和计算机断层扫描(CT)血管造影,结果显示所有冠状动脉均扩张且迂曲,冠状动脉之间存在弥漫性侧支循环。此外,由于LAD起源于肺动脉,我们诊断为“肺动脉起源异常左冠状动脉”(ALCAPA)综合征。我们采用左乳内动脉 - 左前降支动脉(LIMA - LAD)移植术对该患者进行了治疗。