Carminati M, Borghi A, Valsecchi O, Quattrociocchi M, Balduzzi A, Rusconi P, Russo M G, Festa P, Preda L, Tiraboschi R
Department of Cardiology, Ospedali Riuniti, Bergamo, Italy.
Pediatr Cardiol. 1990 Jan;11(1):41-3. doi: 10.1007/BF02239546.
Aortopulmonary window coexisting with tetralogy of Fallot (TF) was prospectively diagnosed by two-dimensional (2D) echocardiography and Doppler in an 18-month-old boy; the diagnosis was confirmed by cardiac catheterization and angiocardiography. Surgical correction was performed, but the patient died in the operating room from right ventricular dysfunction. The autopsy showed an adequate surgical repair, but the histologic examination of the lungs demonstrated severe pulmonary vascular disease, which was presumed to be the cause of death.
一名18个月大的男孩经二维超声心动图和多普勒检查前瞻性诊断为主动脉肺动脉窗合并法洛四联症(TF);心脏导管检查和心血管造影证实了诊断。进行了手术矫正,但患者在手术室因右心室功能障碍死亡。尸检显示手术修复充分,但肺部组织学检查显示严重的肺血管疾病,推测这是死亡原因。