Mirshemirani Alireza, Roshanzamir Fatollah, Shayeghi Shahnaz, Mohajerzadeh Leily, Hasas-Yeganeh Shaghayegh
Pediatric Surgery Research Center, Mofid Children's Hospital, Shaheed Beheshti University of Medical Sciences, Tehran, IR Iran.
Iran J Pediatr. 2010 Jun;20(2):229-32.
Diphallus is a rare anomaly and accompanying anomalies vary from bifid scrotum, bladder exstrophy, imperforate anus and colo-rectal anomaly such as duplication, and other associated anomalies.
A 2-day old infant is reported with imperforate anus and complete duplication of recto-sigmoid colon, rectal pouch, doubling of the genitalia with completely formed penis (diphallus), double bladder, urethra and hypospadias. No family history of abnormalities was noted. The patient underwent several operations: laparatory and colostomy at 3rd day of life, and after clinical and paraclinical investigations, cystoplasty, ureteral reimplantation and resection of left phallus were carried out when 4 months old. At the age of 1 year, after colostogram and total colon evaluation, laparatomy, resection of duplicated recto-sigmoid colon, and pull-through was carried out; 3 months later colostomy closure was performed and the patient discharged without complications.
The patients with diphallus have to be examined carefully because of the high incidence of other systemic anomalies. Treatment of diphallus usually includes excision of the duplicated penile structure, its urethra, and repair of associated anomalies.
双阴茎是一种罕见的畸形,其伴随的畸形包括阴囊裂、膀胱外翻、肛门闭锁以及结肠直肠畸形如重复畸形等其他相关畸形。
报道了一名2日龄婴儿,患有肛门闭锁、直肠乙状结肠完全重复、直肠袋、生殖器双倍且阴茎完全形成(双阴茎)、双膀胱、尿道下裂。未发现家族异常病史。该患者接受了多次手术:出生第3天进行了剖腹术和结肠造口术,在临床和辅助检查后,4个月大时进行了膀胱成形术、输尿管再植术和左侧阴茎切除。1岁时,在进行结肠造影和全结肠评估后,进行了剖腹术、重复直肠乙状结肠切除术和拖出术;3个月后进行了结肠造口闭合术,患者出院,无并发症。
由于其他全身畸形的发生率较高,双阴茎患者必须进行仔细检查。双阴茎的治疗通常包括切除重复的阴茎结构及其尿道,并修复相关畸形。