伴有管状后肠重复畸形的肛门直肠畸形

Anorectal malformation with tubular hindgut duplication.

作者信息

Craigie Ross J, Abbaraju Jaya S, Ba'ath Muhammad E, Turnock Richard R, Baillie Colin T

机构信息

Department of Paediatric Surgery, Royal Liverpool Children's Hospital, Alder Hey, Liverpool L12 2AP, UK.

出版信息

J Pediatr Surg. 2006 Jun;41(6):e31-4. doi: 10.1016/j.jpedsurg.2006.02.038.

DOI:10.1016/j.jpedsurg.2006.02.038

PMID:16769326

Abstract

The association of hindgut duplication and anorectal malformation is rare. Published classifications of this association are confusing in respect of terminology. We report a case of blind-ending, Y-shaped tubular duplication of the distal hindgut, associated with an anorectal malformation (rectourethral fistula) affecting the colon proper. Surgical options at time of presentation and of reconstructive surgery are discussed. A review and suggested modification of the classifications is presented.

摘要

后肠重复畸形与肛门直肠畸形的关联较为罕见。已发表的关于这种关联的分类在术语方面令人困惑。我们报告了一例远端后肠盲端Y形管状重复畸形病例，该病例伴有影响结肠固有部分的肛门直肠畸形（直肠尿道瘘）。文中讨论了就诊时及重建手术的手术选择。并对分类进行了回顾及提出了修改建议。