Clinic of Pediatric Urology, University of Health Sciences, Van Training and Research Hospital, Van, Turkey
Clinic Pediatric Urology, University of Health Sciences, İzmir Tepecik Training and Research Hospital, İzmir, Turkey
Balkan Med J. 2018 Jul 24;35(4):340-343. doi: 10.4274/balkanmedj.2017.1518. Epub 2018 Mar 28.
Diphallia is a very rare anomaly and seen once in every 5.5 million live births. True diphallia with normal penile structures is extremely rare. Surgical management for patients with complete penile duplication without any penile or urethral pathology is challenging.
A 4-year-old boy presented with diphallia. Initial physical examination revealed first physical examination revealed complete penile duplication, urine flow from both penises, meconium flow from right urethra, and anal atresia. Further evaluations showed double colon and rectum, double bladder, and large recto-vesical fistula. Two cavernous bodies and one spongious body were detected in each penile body. Surgical treatment plan consisted of right total penectomy and end-to-side urethra-urethrostomy. No postoperative complications and no voiding dysfunction were detected during the 18 months follow-up.
Penile duplication is a rare anomaly, which presents differently in each patient. Because of this, the treatment should be individualized and end-to-side urethra-urethrostomy may be an alternative to removing posterior urethra. This approach eliminates the risk of damaging prostate gland and sphincter.
双阴茎是一种非常罕见的异常，每 550 万例活产中仅出现 1 例。具有正常阴茎结构的真性双阴茎极为罕见。对于没有任何阴茎或尿道病变的完全性阴茎重复畸形患者，手术管理极具挑战性。
一名 4 岁男孩因双阴茎就诊。初次体格检查显示完全性阴茎重复，尿液从两个阴茎流出，大便从右侧尿道流出，肛门闭锁。进一步评估显示双结肠和直肠、双膀胱和巨大直肠膀胱瘘。每个阴茎体中均检测到两个海绵体和一个海绵体。手术治疗计划包括右侧全阴茎切除术和端侧尿道-尿道吻合术。在 18 个月的随访中，未发现术后并发症和排尿功能障碍。
阴茎重复是一种罕见的异常，在每个患者中的表现均不同。因此，治疗应个体化，端侧尿道-尿道吻合术可能是去除后尿道的一种替代方法。这种方法消除了损伤前列腺和括约肌的风险。
