Peters Matthew N, Katz Morgan J, Alkadri Mohi E
Department of Internal Medicine, Tulane University Health Sciences Center, New Orleans, Louisiana (Peters, Katz); and the Department of Cardiology, Ochsner Medical Center, Jefferson, Louisiana (Alkadri).
Proc (Bayl Univ Med Cent). 2012 Oct;25(4):349-53. doi: 10.1080/08998280.2012.11928874.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an infrequently diagnosed condition with a high incidence of sudden cardiac death. While the only option for cure is orthotopic cardiac transplantation, the use of an implantable cardiac defibrillator can be life saving. Accordingly, the prompt recognition of ARVC is crucial. Fortunately, a definitive diagnosis of ARVC can often be made by a combination of the clinical history and electrocardiogram alone, as illustrated by the present case. In our patient, who presented with multiple syncopal episodes and in whom ventricular tachycardia was observed shortly after her admission to the emergency department, a lengthy and expensive workup was initiated, which ultimately may have delayed implantation of an implantable cardiac defibrillator. Clinicians should be made aware of the clinical guidelines for dealing with this potentially dangerous condition so that appropriate therapy can be promptly initiated.
致心律失常性右室心肌病（ARVC）是一种诊断不常见但心脏性猝死发生率很高的疾病。虽然唯一的治愈方法是原位心脏移植，但植入式心脏除颤器的使用可以挽救生命。因此，及时识别ARVC至关重要。幸运的是，正如本病例所示，通常仅通过临床病史和心电图相结合就能对ARVC做出明确诊断。在我们的患者中，她出现了多次晕厥发作，在急诊科入院后不久就观察到了室性心动过速，于是启动了漫长且昂贵的检查，这最终可能延迟了植入式心脏除颤器的植入。临床医生应了解处理这种潜在危险疾病的临床指南，以便能及时开始适当的治疗。
