Zandecki Lukasz, Sadowski Marcin, Kurzawski Jacek, Janion-Sadowska Agnieszka
Świętokrzyskie Cardiology Center, Provincial Hospital Complex, Kielce, Poland.
Postepy Kardiol Interwencyjnej. 2013;9(3):256-61. doi: 10.5114/pwki.2013.37505. Epub 2013 Sep 16.
Arrhythmogenic right ventricular cardiomyopathy is an infrequently diagnosed, genetically determined disease that leads to significant clinical consequences, including progressive heart failure and ventricular arrhythmias accounting for sudden cardiac death. We report the case of a 52-year-old patient who presented with ventricular tachycardia and features of an acute coronary syndrome. However, routine tests excluded critical coronary stenosis and the final diagnosis was arrhythmogenic right ventricular cardiomyopathy.
致心律失常性右室心肌病是一种诊断率较低的、由基因决定的疾病,可导致严重的临床后果,包括进行性心力衰竭和室性心律失常,后者可导致心源性猝死。我们报告一例52岁患者,其表现为室性心动过速和急性冠状动脉综合征的特征。然而,常规检查排除了严重冠状动脉狭窄,最终诊断为致心律失常性右室心肌病。