Levart Tanja Kersnik, Klokocovnik Tomislav
Departments of Pediatric Nephrology, University Medical Centre Ljubljana, 1525 Ljubljana, Slovenia.
Tex Heart Inst J. 2012;39(5):657-61.
Mid-aortic syndrome, an uncommon acquired or congenital condition characterized by segmental narrowing of the abdominal or distal descending thoracic aorta, is frequently accompanied by ostial stenosis of the aorta's branches. If left untreated, it can result in life-threatening complications secondary to severe hypertension.We report the case of a 3-year-old girl with congenital mid-aortic syndrome, who was diagnosed by chance in the course of a viral illness, and whose high blood pressure values were first dismissed as inaccurate. Attempts to achieve medical or endovascular control of her hypertension were unsuccessful. She was thereafter successfully treated by aorto-aortic bypass grafting, resection of the stenotic segments of both renal arteries, and implantation of the patent arterial segments into the graft.
中段主动脉综合征是一种罕见的后天性或先天性疾病,其特征为腹主动脉或胸降主动脉远端节段性狭窄,常伴有主动脉分支开口处狭窄。若不治疗,可因严重高血压引发危及生命的并发症。我们报告一例3岁先天性中段主动脉综合征女童病例,她在一次病毒感染病程中偶然被诊断出来,其高血压值起初被认为不准确而未予重视。尝试通过药物或血管内介入控制其高血压均未成功。此后,她通过主动脉-主动脉旁路移植术、切除双侧肾动脉狭窄段并将通畅的动脉段植入移植物而获得成功治疗。