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共同肺静脉闭锁中的自发性气胸。

Spontaneous pneumothorax in common pulmonary vein atresia.

作者信息

Sharda J K, Kurlandsky L E, Lacina S J, Radecki L L

机构信息

Gerber Regional Neonatal Intensive Care Unit, Butterworth Hospital, Grand Rapids, Michigan.

出版信息

J Perinatol. 1990 Mar;10(1):70-4.

PMID:2313397
Abstract

Common pulmonary vein atresia is a rare congenital anomaly that is rapidly fatal unless immediately recognized and corrected by surgical intervention. This article describes three neonates who died with the diagnosis soon after birth. In the constellation of presenting clinical features in each case, the occurrence of early spontaneous pneumothorax was particularly noteworthy. This sign may well be a helpful physiologic marker within the context of suspected congenital heart disease associated with severe pulmonary venous obstruction.

摘要

共同肺静脉闭锁是一种罕见的先天性异常,除非立即通过手术干预识别并纠正,否则会迅速致命。本文描述了三名出生后不久即因该诊断而死亡的新生儿。在每个病例呈现的临床特征组合中,早期自发性气胸的出现尤为值得注意。在怀疑与严重肺静脉梗阻相关的先天性心脏病背景下,这一征象很可能是一个有用的生理学标志物。

相似文献

1
Spontaneous pneumothorax in common pulmonary vein atresia.共同肺静脉闭锁中的自发性气胸。
J Perinatol. 1990 Mar;10(1):70-4.
2
Common pulmonary vein atresia: Importance of immediate recognition and surgical intervention.共同肺静脉闭锁:即刻识别与手术干预的重要性。
J Thorac Cardiovasc Surg. 1982 Mar;83(3):443-8.
3
[Atresia of the common pulmonary vein].[肺总静脉闭锁]
Acta Med Port. 1989 Nov-Dec;2(6):281-4.
4
Common pulmonary vein atresia: report of three cases and review of the literature.共同肺静脉闭锁:三例报告并文献复习
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Atresia of the common pulmonary vein--a rare congenital anomaly.共同肺静脉闭锁——一种罕见的先天性异常。
Congenit Heart Dis. 2008 Nov-Dec;3(6):431-4. doi: 10.1111/j.1747-0803.2008.00225.x.
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[Successful repair of a newborn case with total anomalous pulmonary venous connection presenting hemodynamically common pulmonary vein atresia].[成功修复一例新生儿完全性肺静脉异位连接合并血流动力学常见型肺静脉闭锁病例]
Kyobu Geka. 1997 Apr;50(4):298-301.
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Common pulmonary vein atresia: a successfully corrected case.共同肺静脉闭锁:一例成功矫正病例。
J Cardiovasc Surg (Torino). 1987 Jul-Aug;28(4):395-7.
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Atresia of the common pulmonary vein: report of one case.共同肺静脉闭锁:一例报告。
Pediatrics. 1974 Jul;54(1):62-6.
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Central venous catheter: a journey through the central vein--destination pulmonary vein!中心静脉导管:经中心静脉的旅程——目的地肺静脉!
J Cardiothorac Vasc Anesth. 2007 Aug;21(4):625-6. doi: 10.1053/j.jvca.2006.07.018. Epub 2006 Nov 30.
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Unilateral pulmonary vein atresia.单侧肺静脉闭锁
AJR Am J Roentgenol. 1980 Oct;135(4):667-72. doi: 10.2214/ajr.135.4.667.

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