Khonsari S, Saunders P W, Lees M H, Starr A
J Thorac Cardiovasc Surg. 1982 Mar;83(3):443-8.
Common pulmonary vein atresia is a rare congenital anomaly; all four pulmonary veins drain into a common dilated chamber with no direct connections to the heart or systemic venous system. Since its first description in 1962, 16 cases have been reported. Only four patients were surgically managed and none survived. This communication presents the seventeenth reported case of common pulmonary vein atresia and the only patient whose anomaly was suspected early enough to demand immediate surgical management, with gratifying long-term success. The literature on the subject is reviewed and common features of the anomaly are emphasized to facilitate precise diagnosis, so that a futile search for a nonexistent communicating vein is avoided at the time of operation. This approach has led to the first successful surgical management of this otherwise fatal lesion.
共同肺静脉闭锁是一种罕见的先天性异常；所有四条肺静脉都汇入一个共同的扩张腔室，与心脏或体静脉系统无直接连接。自1962年首次描述以来，已报告16例。仅4例患者接受了手术治疗，无一存活。本文报道了第17例共同肺静脉闭锁病例，也是唯一一名异常被早期怀疑并需要立即进行手术治疗且长期效果良好的患者。对该主题的文献进行了综述，并强调了该异常的共同特征以促进精确诊断，从而避免在手术时徒劳地寻找不存在的交通静脉。这种方法首次成功地对这种原本致命的病变进行了手术治疗。
