Khrabrikov A N
Vestn Otorinolaringol. 1990 Jan-Feb(1):28-31.
The fact that ENT doctors infrequently diagnose hemophilia is explained by their inadequate knowledge of the disease. We examined 35 patients suffering from hemophilia A and 3 patients suffering from hemophilia B. The most frequent ENT pathology in them was relapsing nasal hemorrhages of varying intensity and duration (20 patients). Chronic tonsillitis was identified in 17 hemophiliacs. In 2 patients, angina was aggravated by hemorrhages from the tonsils and life-threatening hemorrhages to the soft tissues of the pharynx, neck and mediastinum which led to airways stenosis. In 3 patients, adenoids of the I degree and in 5 patients, adenoids of the II degree were detected. Among other ENT pathologies mention should be made of deformed nasal septum (13 cases), chronic otitis media (4 cases) and chronic suppurative mesotympanitis (1 case). In summary, the most common ENT disease in hemophiliacs is pathology of the lymphadenoid pharyngeal ring detected in more than half of the patients examined. Taking into consideration the specific and life-threatening pattern of potential complications of this pathology, it is important to choose efficient therapeutic methods.
耳鼻喉科医生很少诊断出血友病这一事实，是由于他们对该疾病的了解不足。我们检查了35例甲型血友病患者和3例乙型血友病患者。他们中最常见的耳鼻喉科病变是不同强度和持续时间的复发性鼻出血（20例患者）。17例血友病患者被诊断为慢性扁桃体炎。2例患者因扁桃体出血导致心绞痛加重，咽部、颈部和纵隔软组织出现危及生命的出血，进而导致气道狭窄。3例患者检测出I度腺样体肥大，5例患者检测出II度腺样体肥大。在其他耳鼻喉科病变中，应提及鼻中隔畸形（13例）、慢性中耳炎（4例）和慢性化脓性中鼓膜炎（1例）。总之，血友病患者中最常见的耳鼻喉科疾病是在超过一半的受检患者中检测到的淋巴腺样咽环病变。考虑到这种病变潜在并发症的特殊性和危及生命的情况，选择有效的治疗方法很重要。
