Choi Kang Kook, Kim Jin Yong, Kim Min Jung, Park Hyojun, Choi Dong Wook, Choi Seong Ho, Heo Jin Seok
Department of Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine, Seoul, Korea.
J Korean Surg Soc. 2012 Nov;83(5):316-20. doi: 10.4174/jkss.2012.83.5.316. Epub 2012 Oct 29.
Blue rubber bleb nevus syndrome (BRBNS) is a rare systemic vascular disorder characterized by multiple venous malformations involving many organs. BRBNS can occur in various organs, but the most frequently involved organs are the skin and gastrointestinal (GI) tract. GI lesions of BRBNS can cause acute or chronic bleeding, and treatment is challenging. Herein, we report a case of GI BRBNS that was successfully treated with a combination of intraoperative endoscopy and radical resection.
蓝色橡皮疱痣综合征(BRBNS)是一种罕见的系统性血管疾病,其特征为多个累及多个器官的静脉畸形。BRBNS可发生于各种器官,但最常受累的器官是皮肤和胃肠道(GI)。BRBNS的胃肠道病变可导致急性或慢性出血,治疗具有挑战性。在此,我们报告一例通过术中内镜检查和根治性切除联合成功治疗的胃肠道BRBNS病例。