Muñoz A K, Berek J S, Fu Y S, Heintz P A
Department of Obstetrics and Gynecology, UCLA School of Medicine, Jonsson Comprehensive Cancer Center.
Gynecol Oncol. 1990 Mar;36(3):380-2. doi: 10.1016/0090-8258(90)90147-d.
Five cases of pelvic hemangiopericytomas are reported. One of these tumors arose from the uterus, and four patients had extrauterine, pelvic hemangiopericytomas. The patient with a primary uterine hemangiopericytomas had only simple excision, and, after 6 years, is alive and free of disease. All four patients with extrauterine, pelvic hemangiopericytomas had incomplete resection of their tumors because of hemorrhage. However, pelvic radiation therapy was then employed in these patients and produced a complete regression in one patient and partial regression in two patients with minimal shrinkage in another patient. The latter patients were reexplored after pelvic radiation and underwent complete resection of their disease. Two patients developed pelvic recurrences at 2 and 9 years, respectively, and these were effectively resected. All four patients are all alive and free of disease 5 to 18 years later. If this lesion is unexpectedly discovered at laparotomy, our experience suggests that the resection should be discontinued and that they should be treated with pelvic radiation and delayed resection of persistent and recurrent pelvic tumors.
本文报告了5例盆腔血管外皮细胞瘤。其中1例肿瘤起源于子宫，另外4例患者患有子宫外盆腔血管外皮细胞瘤。原发性子宫血管外皮细胞瘤患者仅接受了简单切除，6年后仍存活且无疾病。所有4例子宫外盆腔血管外皮细胞瘤患者因出血肿瘤切除不完全。然而，这些患者随后接受了盆腔放射治疗，其中1例患者肿瘤完全消退，2例患者部分消退，另1例患者肿瘤缩小不明显。后一组患者在盆腔放疗后再次接受手术，疾病得以完全切除。2例患者分别在2年和9年后出现盆腔复发，均成功切除。5至18年后，所有4例患者均存活且无疾病。如果在剖腹手术中意外发现这种病变，我们的经验表明应停止切除，而应采用盆腔放疗，并对持续和复发的盆腔肿瘤进行延迟切除。
