Chan S C, Lee C M, Ng Y B, Tsai C H
Department of Diagnostic Radiology, Chang Gung Memorial Hospital, Keelung, Taiwan, ROC.
Postgrad Med J. 1995 Nov;71(841):692-5. doi: 10.1136/pgmj.71.841.692.
Hemangiopericytomas are rare vascular tumours that are derived from pericytes. Retroperitoneal hemangiopericytomas are usually bulky but clinically silent when diagnosed because of their slow rate of growth. A 49-year-old man, who presented with only vague symptoms of abdominal fullness for several months, was found on computed tomography to have a huge well-defined mass with areas of low attenuation and well-enhanced septa. The tumour was successfully resected and was confirmed to be a malignant retroperitoneal hemangiopericytoma. It measured 30 cm in the greatest dimension. We are prompted to present this case as it is believed to be the largest tumour reported to date.
血管外皮细胞瘤是一种罕见的起源于周细胞的血管肿瘤。腹膜后血管外皮细胞瘤通常体积较大,但由于生长缓慢,诊断时临床上往往没有症状。一名49岁男性,仅数月来一直有腹部胀满的模糊症状,计算机断层扫描发现其有一个巨大的边界清晰的肿块,有低密度区和强化良好的分隔。肿瘤被成功切除,经证实为恶性腹膜后血管外皮细胞瘤。其最大直径为30厘米。我们之所以介绍这个病例,是因为它被认为是迄今为止报道的最大的此类肿瘤。