Abroug F, Dougui M, Knani J, Hmouda H, Belghith M, Khouaja F, Bouchoucha S
Service de Réanimation Polyvalente, CHU, Tunisie.
Rev Mal Respir. 1990;7(2):159-61.
The Arnold-Chiari malformation (MAC), ectopic medulla of the cerebral hemispheres, may be the basis of respiratory problems provoked by compression of the respiratory centre. It is associated with numerous respiratory problems in children; there are however few publications related to the association of MAC and ventilatory problems in adults. It was recently suggested and subsequently shown that the syndrome of sleep apnoea (SAS) could occur in relation to MAC. We report a new observation documenting the association of MAC and SAS. The surgical cure of MAC enabling a remission of SAS suggests the existence in this case of a causal relation between the two pathologies. A search for such a malformation by imagery of the occipito-medullary crest should be a part of the work up in SAS when the cause remains undetermined.
阿诺德-奇阿利畸形（MAC），即大脑半球延髓异位，可能是呼吸中枢受压引发呼吸问题的基础。它与儿童的众多呼吸问题相关；然而，关于MAC与成人通气问题关联的出版物很少。最近有人提出并随后证实，睡眠呼吸暂停综合征（SAS）可能与MAC相关。我们报告一例新病例，记录了MAC与SAS的关联。MAC的手术治愈使SAS缓解，提示在该病例中这两种病理之间存在因果关系。当SAS病因不明时，通过枕骨大孔区成像检查这种畸形应作为SAS检查工作的一部分。
