Division of Pulmonary and Critical Care Medicine, Department of Internal Medicine, CHA Bundang Medical Center, College of Medicine, CHA University, Seongnam, South Korea.
Respir Care. 2013 Aug;58(8):e92-4. doi: 10.4187/respcare.01996. Epub 2012 Dec 18.
Primary malignant fibrous histiocytoma (MFH) of the lung is a very rare neoplasm that usually presents as a parenchymal mass. Here we report an unusual case of primary MFH of the bronchus, showing relatively benign clinical features. We performed a palliative resection via flexible bronchoscopy, using a polypectomy snare. The patient has survived for over 2 years after being diagnosed with an endobronchial mass, later found to be MFH, and 14 months post-debulking. There is a possibility that endobronchial MFH has a more favorable prognosis than MFH of other origins. If this is true, interventional bronchoscopy can be a reasonable option for non-operable cases of MFH.
原发性肺恶性纤维组织细胞瘤（MFH）是一种非常罕见的肿瘤，通常表现为实质肿块。在此，我们报告一例支气管原发性 MFH 的不典型病例，其表现出相对良性的临床特征。我们通过软性支气管镜使用息肉切除术圈套器进行姑息性切除。该患者在诊断为支气管内肿块（后证实为 MFH）后已生存超过 2 年，肿块减积术后 14 个月仍存活。支气管内 MFH 的预后可能优于其他起源的 MFH。如果这是真的，那么对于无法手术的 MFH 病例，介入性支气管镜检查可能是一种合理的选择。
