起源于肾包膜的恶性纤维组织细胞瘤：一种极其罕见的实体。

Malignant fibrous histiocytoma arising from renal capsule: An extremely rare entity.

作者信息

Bairwa Shilpa, Sangwaiya Ashok, Ansari Mariyam, Jindal Arpita, Singla Sapna, Yadav Ajay

机构信息

Department of Pathology, SHKM, GMC, Mewat, Haryana, India.

Department of Pathology, SMS, Jaipur, Rajasthan, India.

出版信息

Indian J Pathol Microbiol. 2017 Jul-Sep;60(3):402-404. doi: 10.4103/IJPM.IJPM_810_15.

DOI:10.4103/IJPM.IJPM_810_15

PMID:28937382

Abstract

Malignant fibrous histiocytoma (MFH) usually presents in the extremities or retroperitoneum. MFH arising from renal parenchyma or renal capsule is extremely rare, only few cases have been reported in literature and portend a poor prognosis. Renal MFH is differentiated from renal cell carcinoma, renal sarcoma, and sarcomatoid renal tumor only by histological and immunohistochemical studies. Since the therapeutic options for MFH are different, its early diagnosis is imperative. Herein, we report a case of a primary renal MFH in a 35-year-old male.

摘要

恶性纤维组织细胞瘤（MFH）通常出现在四肢或腹膜后。起源于肾实质或肾包膜的MFH极为罕见，文献中仅报道了少数病例，且预后不佳。肾MFH仅通过组织学和免疫组织化学研究与肾细胞癌、肾肉瘤及肉瘤样肾肿瘤相鉴别。由于MFH的治疗选择不同，早期诊断至关重要。在此，我们报告一例35岁男性原发性肾MFH病例。