Cabezuelo Huerta G, Frontera Izquierdo P
Departamento de Pediatría, Hospital Infantil La Fe, Universidad de Valencia.
Rev Esp Cardiol. 1990 Feb;43(2):93-6.
The results in the management of 36 cases of isolated total anomalous pulmonary venous connection are presented. This patients are the 1.55% of the 2,322 children diagnosed of congenital heart disease by catheterization and angiography in our hospital at the 1971-1988 period. Nineteen had a type I, five a type II, eight a type III and four a mixed type lesion. The total mortality rate was 63.8%. Twenty six infants underwent surgical correction at a mean age of 2.5 months with an operative mortality rate of the 57.7%. Eleven infants survived operation. There have been no late deaths but one children developed stenosis at the anastomosis. The final actuarial survival rate was the 34.4% in the total group and the 42.3% in the operated group. The strongest determinants of survival were the type of lesion and pulmonary venous obstruction. No improving in the total and the surgical results has been observed in the last 10 years.
本文报告了36例孤立性完全性肺静脉异位连接的治疗结果。这些患者占我院1971 - 1988年期间经心导管检查和血管造影确诊为先天性心脏病的2322例儿童的1.55%。其中19例为I型，5例为II型，8例为III型，4例为混合型病变。总死亡率为63.8%。26例婴儿平均在2.5个月时接受了手术矫正，手术死亡率为57.7%。11例婴儿术后存活。无晚期死亡病例，但有1例患儿吻合口出现狭窄。全组最终精算生存率为34.4%，手术组为42.3%。生存的最强决定因素是病变类型和肺静脉梗阻。在过去10年中，总体和手术结果均未观察到改善。
