一名新生儿的快速致命性多器官朗格汉斯细胞组织细胞增多症
Rapidly fatal multiorgan Langerhans cell histiocytosis in a neonate.
作者信息
Gee Sarah N, Huang Jennifer T, Schmidt Birgitta A, Gellis Stephen E
机构信息
Harvard Combined Program in Dermatology, Boston, Massachusetts.
出版信息
Pediatr Dermatol. 2013 Sep-Oct;30(5):e85-6. doi: 10.1111/pde.12050. Epub 2012 Dec 26.
PMID:23278554
Abstract
Multiorgan Langerhans cell histiocytosis (LCH) presenting in the neonatal period is associated with a poor prognosis. We report a 5-day-old neonate who presented at birth with diffuse cutaneous nodules and respiratory failure who received a postmortem diagnosis of LCH. We emphasize the importance of recognizing the cutaneous findings of this rare disease.
摘要
新生儿期出现的多器官朗格汉斯细胞组织细胞增多症（LCH）预后较差。我们报告一例5日龄新生儿，出生时即表现为弥漫性皮肤结节和呼吸衰竭，尸检诊断为LCH。我们强调认识这种罕见疾病皮肤表现的重要性。
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